Aldurazyme 100 U/mL is an enzyme replacement therapy (ERT) used for the treatment of Mucopolysaccharidosis I (MPS I), a rare genetic disorder caused by the deficiency of the enzyme alpha-L-iduronidase. Manufactured by Sanofi, Aldurazyme helps reduce the buildup of glycosaminoglycans (GAGs) in the body’s cells, improving organ function and quality of life for MPS I patients.
What is Aldurazyme 100 U/mL?
Aldurazyme 100 U/mL (Laronidase) is a highly specialized enzyme replacement therapy (ERT) designed to treat Mucopolysaccharidosis Type I (MPS I), a progressive and life-threatening disorder. Patients with MPS I experience a buildup of complex sugars (GAGs), leading to organ dysfunction, joint stiffness, and respiratory complications. Aldurazyme effectively reduces these accumulations, alleviating symptoms and slowing disease progression.
How Does Aldurazyme Work?
Aldurazyme contains Laronidase, a recombinant form of the human enzyme alpha-L-iduronidase, which is responsible for breaking down glycosaminoglycans (GAGs). By supplementing this missing enzyme, Aldurazyme helps:
✔️ Reduce organ enlargement (liver & spleen)
✔️ Improve joint mobility & flexibility
✔️ Enhance lung function & breathing capacity
✔️ Reduce GAG storage in cells
Who Should Use Aldurazyme 100 U/mL?
Aldurazyme is prescribed for individuals diagnosed with Mucopolysaccharidosis Type I (MPS I), including its three major forms:
✔️ Hurler syndrome (severe MPS I)
✔️ Hurler-Scheie syndrome (moderate MPS I)
✔️ Scheie syndrome (mild MPS I)
Administration & Dosage
- Form: Injectable concentrate for intravenous infusion
- Dosage: Typically administered once per week at a dose of 0.58 mg/kg
- Route: Intravenous (IV) infusion, given under medical supervision
- Infusion Duration: Generally 3-4 hours, depending on patient tolerance
Potential Side Effects
While Aldurazyme 100 U/mL is well-tolerated, some patients may experience mild to moderate infusion-related reactions, such as:
✔️ Fever & chills
✔️ Nausea & vomiting
✔️ Skin rashes
✔️ Respiratory issues (cough or shortness of breath)
Severe allergic reactions are rare but possible; therefore, medical professionals monitor patients closely during administration.
Why Choose Aldurazyme 100 U/mL?
🔹 Only FDA-approved enzyme therapy for MPS I
🔹 Clinically proven to improve organ function and reduce GAG accumulation
🔹 Manufactured by Sanofi, a leader in rare disease treatments
🔹 Proven safety profile with long-term benefits
Buy Aldurazyme 100 U/mL at the Best Price
At Etica Pharmacy, we offer Aldurazyme 100 U/mL (Laronidase) at competitive prices with worldwide shipping. Contact us today for bulk orders, prescription verification, and delivery options.
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